D81Combined immunodeficiencies
ICD-10-CM category (non-billable header) code — part of Certain disorders involving the immune mechanism (D80-D89)
Coding Notes
Excludes1 (never code both together)
- autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
Subcategories (10)
- D81.0 Severe combined immunodeficiency with reticular dysgenesis
- D81.1 Severe combined immunodeficiency w low T- and B-cell numbers
- D81.2 Severe combined immunodef w low or normal B-cell numbers
- D81.3 Adenosine deaminase [ADA] deficiency
- D81.4 Nezelof's syndrome
- D81.5 Purine nucleoside phosphorylase [PNP] deficiency
- D81.6 Major histocompatibility complex class I deficiency
- D81.7 Major histocompatibility complex class II deficiency
- D81.8 Other combined immunodeficiencies
- D81.9 Combined immunodeficiency, unspecified