| Full description | Disorder of branched-chain amino-acid metabolism, unspecified |
| Billable | Yes |
| Chapter | Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E89) |
| Section | Metabolic disorders (E70-E88) |
| Parent code | E71 — Disord of branched-chain amino-acid metab & fatty-acid metab |