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Ch. 4: Endocrine, nutritional and metabolic diseases (E00-E89)
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Metabolic disorders (E70-E88)
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E71 Disord of branched-chain amino-acid metab & fatty-acid metab
› E71.4
E71.4
Disorders of carnitine metabolism
ICD-10-CM category (non-billable header) code — part of Metabolic disorders (E70-E88)
Code Details
Billable
No — use a more specific child code
Chapter
Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E89)
Section
Metabolic disorders (E70-E88)
Parent code
E71 — Disord of branched-chain amino-acid metab & fatty-acid metab
Coding Notes
Excludes1 (never code both together)
Muscle carnitine palmitoyltransferase deficiency (E71.314)
Subcategories (5)
E71.40
Disorder of carnitine metabolism, unspecified
E71.41
Primary carnitine deficiency
E71.42
Carnitine deficiency due to inborn errors of metabolism
E71.43
Iatrogenic carnitine deficiency
E71.44
Other secondary carnitine deficiency
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