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Ch. 4: Endocrine, nutritional and metabolic diseases (E00-E89)
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Metabolic disorders (E70-E88)
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E71 Disord of branched-chain amino-acid metab & fatty-acid metab
› E71.5
E71.5
Peroxisomal disorders
ICD-10-CM category (non-billable header) code — part of Metabolic disorders (E70-E88)
Code Details
Billable
No — use a more specific child code
Chapter
Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E89)
Section
Metabolic disorders (E70-E88)
Parent code
E71 — Disord of branched-chain amino-acid metab & fatty-acid metab
Coding Notes
Excludes1 (never code both together)
Schilder's disease (G37.0)
Subcategories (5)
E71.50
Peroxisomal disorder, unspecified
E71.51
Disorders of peroxisome biogenesis
E71.52
X-linked adrenoleukodystrophy
E71.53
Other group 2 peroxisomal disorders
E71.54
Other peroxisomal disorders
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