E75Disord of sphingolipid metab and oth lipid storage disorders
ICD-10-CM category (non-billable header) code — part of Metabolic disorders (E70-E88)
Coding Notes
Excludes1 (never code both together)
- mucolipidosis, types I-III (E77.0-E77.1)
- Refsum's disease (G60.1)
Subcategories (7)
- E75.0 GM2 gangliosidosis
- E75.1 Other and unspecified gangliosidosis
- E75.2 Other sphingolipidosis
- E75.3 Sphingolipidosis, unspecified
- E75.4 Neuronal ceroid lipofuscinosis
- E75.5 Other lipid storage disorders
- E75.6 Lipid storage disorder, unspecified