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Ch. 4: Endocrine, nutritional and metabolic diseases (E00-E89)
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Metabolic disorders (E70-E88)
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E76 Disorders of glycosaminoglycan metabolism
› E76.0
E76.0
Mucopolysaccharidosis, type I
ICD-10-CM category (non-billable header) code — part of Metabolic disorders (E70-E88)
Code Details
Billable
No — use a more specific child code
Chapter
Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E89)
Section
Metabolic disorders (E70-E88)
Parent code
E76 — Disorders of glycosaminoglycan metabolism
Subcategories (3)
E76.01
Hurler's syndrome
E76.02
Hurler-Scheie syndrome
E76.03
Scheie's syndrome
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