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Ch. 4: Endocrine, nutritional and metabolic diseases (E00-E89)
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Metabolic disorders (E70-E88)
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E76.2 Other mucopolysaccharidoses
› E76.22
E76.22
Sanfilippo mucopolysaccharidoses
ICD-10-CM billable/specific code — part of Metabolic disorders (E70-E88)
Code Details
Billable
Yes
Chapter
Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E89)
Section
Metabolic disorders (E70-E88)
Parent code
E76.2 — Other mucopolysaccharidoses
Coding Notes
Inclusion Terms
Mucopolysaccharidosis, type III (A) (B) (C) (D)
Sanfilippo A syndrome
Sanfilippo B syndrome
Sanfilippo C syndrome
Sanfilippo D syndrome
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