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Ch. 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
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Other congenital malformations (Q80-Q89)
› Q80
Q80
Congenital ichthyosis
ICD-10-CM category (non-billable header) code — part of Other congenital malformations (Q80-Q89)
Code Details
Billable
No — use a more specific child code
Chapter
Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Section
Other congenital malformations (Q80-Q89)
Coding Notes
Excludes1 (never code both together)
Refsum's disease (G60.1)
Subcategories (7)
Q80.0
Ichthyosis vulgaris
Q80.1
X-linked ichthyosis
Q80.2
Lamellar ichthyosis
Q80.3
Congenital bullous ichthyosiform erythroderma
Q80.4
Harlequin fetus
Q80.8
Other congenital ichthyosis
Q80.9
Congenital ichthyosis, unspecified
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