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Ch. 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
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Other congenital malformations (Q80-Q89)
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Q82 Other congenital malformations of skin
› Q82.2
Q82.2
Congenital cutaneous mastocytosis
ICD-10-CM billable/specific code — part of Other congenital malformations (Q80-Q89)
Code Details
Billable
Yes
Chapter
Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Section
Other congenital malformations (Q80-Q89)
Parent code
Q82 — Other congenital malformations of skin
Coding Notes
Inclusion Terms
Congenital diffuse cutaneous mastocytosis
Congenital maculopapular cutaneous mastocytosis
Congenital urticaria pigmentosa
Excludes1 (never code both together)
cutaneous mastocytosis NOS (D47.01)
diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
malignant mastocytosis (C96.2-)
systemic mastocytosis (D47.02)
urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
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