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Ch. 4: Endocrine, nutritional and metabolic diseases (E00-E89)
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Metabolic disorders (E70-E88)
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E75.2 Other sphingolipidosis
› E75.24
E75.24
Niemann-Pick disease
ICD-10-CM category (non-billable header) code — part of Metabolic disorders (E70-E88)
Code Details
Billable
No — use a more specific child code
Chapter
Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E89)
Section
Metabolic disorders (E70-E88)
Parent code
E75.2 — Other sphingolipidosis
Coding Notes
Inclusion Terms
Acid sphingomyelinase deficiency (ASMD)
Subcategories (7)
E75.240
Niemann-Pick disease type A
E75.241
Niemann-Pick disease type B
E75.242
Niemann-Pick disease type C
E75.243
Niemann-Pick disease type D
E75.244
Niemann-Pick disease type A/B
E75.248
Other Niemann-Pick disease
E75.249
Niemann-Pick disease, unspecified
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