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Ch. 4: Endocrine, nutritional and metabolic diseases (E00-E89)
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Metabolic disorders (E70-E88)
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E75.24 Niemann-Pick disease
› E75.240
E75.240
Niemann-Pick disease type A
ICD-10-CM billable/specific code — part of Metabolic disorders (E70-E88)
Code Details
Billable
Yes
Chapter
Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E89)
Section
Metabolic disorders (E70-E88)
Parent code
E75.24 — Niemann-Pick disease
Coding Notes
Inclusion Terms
Acid sphingomyelinase deficiency type A (ASMD type A)
Infantile neurovisceral acid sphingomyelinase deficiency
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